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Medical Moments

Acute Groups
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Medical Moment:
In an individual with an acute porphyria, an acute attack can be brought on by certain drugs, hormones in women, environmental factors including chemicals of various types, nutrition including fasting and low carbohydrate diets, alcoholic beverages, medical and physical stress, and physical fatigue.
What factors precipitate an acute porphyria attack for you? Comment below.
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Cutaneous Groups:
Medical Moment:
Sun sensitivity is the main symptom in CEP, EPP, XLP and PCT. VP and HCP, which are acute porphyrias, can also have blistering sun sensitivity. The degree of sensitivity to sunlight varies considerably. Patients with sun sensitivity have high levels of porphyrins in the blood plasma which, depending on the type of porphyria, have originated from the liver or the bone marrow. Ultraviolet light interacts with porphyrins in such a way as to damage skin tissue. In general, patients with CEP, EPP, XLP and PCT should protect themselves to prevent sun exposure and patients with VP or HCP should also protect themselves if this is one of their symptoms.
What do you do to protect yourself from the sunlight? Comment below.

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